Search results for "pseudoxanthoma elasticum"
showing 7 items of 7 documents
Scanning electron microscopic and X ray microanalysis study of the mineral deposits in pseudoxanthoma elasticum.
1977
A skin biopsy of a 37 year old man with typical lesions of pseudoxanthoma clasticum (P.E.) associated with angioid streaks (Groenblad-Strandberg Syndrom) was examined with a scanning E. M. (SEM) and a SEM provided with a X ray micro-analyser. The SEM provided with X ray microanalyser enabled us to see the correspondence between the crystalline deposits and a calcium salt. The potassium, sodium and magnesium analysis of the specimen permits us to verify that the P.E. dermis is rich in K and poor in Mg.
Autofluorescence Imaging of the Skin Is an Objective Non-Invasive Technique for Diagnosing Pseudoxanthoma Elasticum
2021
Pseudoxanthoma elasticum (PXE) is a rare multisystemic autosomal recessive connective tissue disease. In most cases, skin manifestations of PXE are the first to develop, followed later by severe ocular and cardiovascular complications. In our present study, in addition to dermoscopy, we introduced novel techniques, autofluorescence (AF) and diffuse reflectance (DR) imaging for the assessment of affected skin sites of five PXE patients. PXE-affected skin areas in most skin sites showed a previously observed pattern upon dermoscopic examination. With the novel imaging, PXE-affected skin lesions displayed high AF intensity. During our measurements, significantly higher mean, minimum and maximu…
Zur Frage humoraler Kollagen-Begleitkomponenten beim Pseudoxanthoma elasticum
1968
Bei einer 24jahrigen Kranken mit Pseudoxanthoma exsudativum werden bei eingehender, vor allem auch laboratoriumsmasiger Durchuntersuchung eine Herabsetzung der Hydroxyprolin-Ausscheidung und eine Vermehrung der Mucopolysaccharid-Ausscheidung im Urin festgestellt. Diese beiden Befunde entsprechen Ergebnissen, wie man sie nach vorangehenden eigenen Untersuchungen auch bei diffusen Bindegewebskrankheiten bzw. speziell bei progressiver Sklerodermie findet. Diese Resultate konnen somit als humoral fasbare Kollagen-Begleitkomponenten bei diesem Leiden gelten. Unter diesem Gesichtspunkt ware das Pseudoxanthoma elasticum mithin nicht nur eine systematisierte Elastose, sondern eher eine Kollagenoela…
089 Autofluorescence imaging for non-invasive visualization and quantification of skin lesions of patients with pseudoxanthoma elasticum
2021
[Pseudoxanthoma elasticum (Grönblad-Strandberg syndrome) and rheumatoid arthritis].
1990
A 72-year-old woman, not previously known to have coronary heart disease, was admitted to hospital with an acute anterior wall myocardial infarction. The history revealed that, when about 40 years of age, a coarse skin-fold and yellowish-white xanthoma-like efflorescences had been noted around her umbilicus, the inguinal regions and axillae. These changes subsequently developed into a pathognomonic picture of pseudoxanthoma elasticum (PE), which was a significant factor in the myocardial infarction. At the age of 69 years, rheumatoid arthritis (RA), stage II after Steinbrocker, had been diagnosed on the basis of morning stiffness, symmetrical arthritis in more than three joint regions and t…
Automated macular choroidal thickness measurement by swept-source optical coherence tomography in pseudoxanthoma elasticum
2016
Introduction Pseudoxanthoma elasticum (PXE) typically involves elastic fibers in blood vessels and Bruch membrane. Our purpose was to analyze retinal and choroidal macular thickness in patients with angioid streaks due PXE compared with a control group. Methods Best-corrected visual acuity (BCVA), axial length (AL), and macular swept-source optical coherence tomography were obtained. Automated segmentations of the retina and the choroid were used to obtain the corresponding thickness values. An age, gender and AL matched control group was used to compare the thickness values. Results Twelve eyes of 6 patients were included. The mean BCVA was 0.68 ± 0.29 versus 1.0 in controls (p < 0.001). T…